Breast Ewing Sarcoma/Primitive Neuroectodermal Tumor: A Case Report and a Review of the Literature
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چکیده
Extraskeletal Ewing’s Sarcoma is a rare soft tissue tumor that is morphologically indistinguishable from the more common Ewing’s sarcoma of the bone. Primitive Ewing’s sarcoma of the breast is exceptionally reported. We present the case of a 26-year-old woman with Ewing sarcoma/PNET diagnosed by molecular biology showing the specific t ranscr ipt of Ewing/ per ipheral pr imi t ive neuroectodermal tumor (pPNET). A definitive diagnosis of primary Ewing sarcoma/PNET of the breast was made following a negative staging evaluation.
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Peripheral Primitive Neuroectodermal Tumor of the Pelvis
The primitive neuroectodermal tumor (PNET) belongs to a group of highly malignant tumors and is composed of small round cells of a neuroectodermal origin. Categorized in the same tumor family as Ewing sarcoma, the PNET is most likely to occur in bones and soft tissues. However, a small number of PNET cases arising in the pelvis have been reported as well. We present three cases of pelvic PNET: ...
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